Case Reports
Idiopathic retroperitoneal fibrosis in a young female; the first case report in Sri Lanka
Authors:
Pradeep Jayantha Gamage ,
Provincial General Hospital Badulla, Badulla, LK
Saman Chandana,
Provincial General Hospital, Badulla, LK
Upul Weerasinghe,
Provincial General Hospital, Badulla, LK
Mohan Samarasinghe,
Provincial General Hospital, Badulla, LK
Sampath Jayawardhane,
Provincial General Hospital, Badulla, LK
Nadun Dhanushka Gamage,
Provincial General Hospital, Badulla, LK
Jalitha Thinnarachchi
Provincial General Hospital, Badulla, LK
Abstract
Idiopathic retroperitoneal fibrosis (IRF) is a rare disease with a better prognosis if identified earlier and treated promptly. This is thought to be secondary to an autoimmune process resulting in fibrosis, causing obstructive uropathy. Radiological aspects play a major role in diagnosis and follow up. We present a young female patient who was diagnosed with idiopathic retroperitoneal fibrosis and treated successfully. This case highlights the fact that diagnosing IRF is a result of a cascade of reasonable investigations and early diagnosis prevents irreversible renal damage. Classic radiological features with histology provide a guide to the proper diagnosis, and treatment with corticosteroids gives a marked response.
How to Cite:
Gamage, P.J., Chandana, S., Weerasinghe, U., Samarasinghe, M., Jayawardhane, S., Gamage, N.D. and Thinnarachchi, J., 2018. Idiopathic retroperitoneal fibrosis in a young female; the first case report in Sri Lanka. Sri Lanka Journal of Medicine, 27(2), pp.59–62. DOI: http://doi.org/10.4038/sljm.v27i2.94
Published on
26 Dec 2018.
Peer Reviewed
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